Fetal acalvaria with amniotic band syndrome
Suresh Chandrana, Meng Keang Lima, Victor Yu-Hei Yub
a Special Care Baby
unit, Department of
Paediatrics, RIPAS Hospital,
Bandar Seri Begawan,
Brunei Darussalam, b Neonatal Intensive Care
Unit, Monash Medical Centre,
Victoria, Australia
Correspondence to: Dr Suresh Chandran Email: sunitha{at}brunet.bn
Accepted 26 June 1999
A case of amniotic band syndrome (ABS) presenting with
acalvaria is reported. ABS includes a spectrum of non-genetic
anomalies, varying from simple digital band constriction to major
craniofacial and visceral defects, and even fetal death. Acalvaria is a
rare congenital malformation characterised by the absence of the
dome-like superior portion of the cranium comprising the frontal,
parietal, and occipital bones and dura mater, in the presence of a
normal skull base and facial bones with complete cranial contents. No two cases are the same. Acrania or absence of the flat skull bones with
disorganised cerebral hemispheres have been reported in the presence of
amniotic bands. ABS is an aetiological factor in acalvaria. Appropriate
counselling for affected families needs to be given after prenatal diagnosis.
Keywords: acalvaria; acrania; amniotic band syndrome
© 2000 by Archives of Disease in Childhood
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This article has been cited by other articles:
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Raines, C.
(2006). Primary Acalvaria. Journal of Diagnostic Medical Sonography
22: 407-410
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